Prevalence study of primary dystonia in Iceland

• Published in: Movement Disorders
• Main Authors: Asgeirsson, Hilmir, Jakobsson, Finnbogi, Hjaltason, Haukur, Jonsdottir, Helga, Sveinbjornsdottir, Sigurlaug
• Format: Article in Journal/Newspaper
• Language: English
• Published: Wiley-Liss 2006
• Subjects: Adult; Age Distribution; Dystonic Disorders; Female; Humans; Iceland/epidemiology; Male; Middle Aged; Prevalence; Sex Distribution; Iceland
• Online Access: http://hdl.handle.net/2336/6499; https://doi.org/10.1002/mds.20674

To access publisher full text version of this article. Please click on the hyperlink in Additional Link field In Iceland, the crude prevalence for all types of primary dystonia was 37.1/10(5) (confidence interval, 30.4-44.9). Focal dystonia had the highest prevalence (31.2/10(5)), followed by segmental (3.1/10(5)), multifocal (2.4/10(5)) and generalized dystonia (0.3/10(5)). Cervical dystonia was the most common focal dystonia (11.5/10(5)), followed by limb dystonia (8.0/10(5)), laryngeal dystonia (5.9/10(5)), blepharospasm (3.1/10(5)), and oromandibular dystonia (2.8/10(5)). The male:female ratio for all patients was 1:1.9 (P=0.0007), and females outnumbered males in all subtypes except oromandibular dystonia. Mean age of onset for all patients was 42.7 years (range, 3-82 years). This prevalence of primary dystonia is higher than in most reported studies, possibly because of more complete ascertainment but the relative frequencies of dystonia subtypes is similar.