Congenital cardiac malformations in Iceland from 1990 through 1999
To access publisher full text version of this article. Please click on the hyperlink in Additional Links field INTRODUCTION AND BACKGROUND: About 1% of live-born children have congenital malformations of the heart. The aim of our study was to investigate the incidence of such defects in children bor...
Published in: | Cardiology in the Young |
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Online Access: | http://hdl.handle.net/2336/32892 https://doi.org/10.1017/S1047951104004081 |
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ftlandspitaliuni:oai:www.hirsla.lsh.is:2336/32892 2023-05-15T16:47:14+02:00 Congenital cardiac malformations in Iceland from 1990 through 1999 Stephensen, Sigurdur Sverrir Sigfusson, Gunnlaugur Eiriksson, Herbert Sverrisson, Jon Thor Torfason, Bjarni Haraldsson, Asgeir Helgason, Hrodmar Children's Hospital, University Hospital of Iceland, Hringbraut, Reykjavik, Iceland. 2008-07-23 http://hdl.handle.net/2336/32892 https://doi.org/10.1017/S1047951104004081 en eng Cambridge University Press http://search.ebscohost.com/login.aspx?direct=true&db=aph&AN=16824970&site=ehost-live Cardiol Young 2004, 14(4):396-401 1047-9511 15680046 doi:10.1017/S1047951104004081 http://hdl.handle.net/2336/32892 Cardiology in the young Cardiac Surgical Procedures Coronary Angiography Echocardiography Doppler Electrocardiography Female Heart Catheterization Heart Defects Congenital Humans Iceland Incidence Infant Newborn Male Registries Retrospective Studies Risk Assessment Severity of Illness Index Sex Distribution Survival Rate Article 2008 ftlandspitaliuni https://doi.org/10.1017/S1047951104004081 2022-05-29T08:21:10Z To access publisher full text version of this article. Please click on the hyperlink in Additional Links field INTRODUCTION AND BACKGROUND: About 1% of live-born children have congenital malformations of the heart. The aim of our study was to investigate the incidence of such defects in children born in Iceland during a period of 10 years, extending from 1990 through 1999. MATERIALS AND METHODS: Information about the patients was obtained from medical records from two hospitals that cover the whole country, a private clinic of pediatric cardiologists, an echocardiography database, autopsy reports, and death certificates. We investigated the distribution of specific malformations, the age at diagnosis, the symptoms leading to the diagnosis, the source of referral, and treatment and quality of life. RESULTS: Between 1990 and 1999, there were 44,013 live births in Iceland, of which 740 patients were diagnosed with congenital cardiac malformations, accounting for 1.7% of the live-born children. The distribution was made up of 338 patients with ventricular septal defect (45.7%), 90 with atrial septal defect (12.2%), 85 with patency of the arterial duct (11.5%), 48 with pulmonary valvar stenosis (6.5%), 38 with a bicuspid aortic valve (5.1%), 28 with aortic coarctation (3.8%), 22 with tetralogy of Fallot (3.0%), 14 with transposed great arteries (1.9%), 11 with aortic stenosis (1.5%), 10 with atrioventricular septal defect and common atrioventricular orifice (1.4%), 9 with mitral valvar regurgitation (1.2%), 7 with sub-aortic stenosis (0.9%), and 5 with hypoplasia of the left heart (0.7%). Extracardiac anomalies were seen in 89 patients (12.0%). Chromosomal defects were seen in 36 patients, of whom 28 had Down's syndrome. DISCUSSION: The annual incidence of diagnosis of patients with congenital cardiac malformations increased during the period of study. This was noted for minor defects, but the incidence of the major anomalies did not alter. Our observed yearly incidence, at 1.7%, was higher than noted in a previous ... Article in Journal/Newspaper Iceland Hirsla - Landspítali University Hospital research archive Cardiology in the Young 14 4 396 401 |
institution |
Open Polar |
collection |
Hirsla - Landspítali University Hospital research archive |
op_collection_id |
ftlandspitaliuni |
language |
English |
topic |
Cardiac Surgical Procedures Coronary Angiography Echocardiography Doppler Electrocardiography Female Heart Catheterization Heart Defects Congenital Humans Iceland Incidence Infant Newborn Male Registries Retrospective Studies Risk Assessment Severity of Illness Index Sex Distribution Survival Rate |
spellingShingle |
Cardiac Surgical Procedures Coronary Angiography Echocardiography Doppler Electrocardiography Female Heart Catheterization Heart Defects Congenital Humans Iceland Incidence Infant Newborn Male Registries Retrospective Studies Risk Assessment Severity of Illness Index Sex Distribution Survival Rate Stephensen, Sigurdur Sverrir Sigfusson, Gunnlaugur Eiriksson, Herbert Sverrisson, Jon Thor Torfason, Bjarni Haraldsson, Asgeir Helgason, Hrodmar Congenital cardiac malformations in Iceland from 1990 through 1999 |
topic_facet |
Cardiac Surgical Procedures Coronary Angiography Echocardiography Doppler Electrocardiography Female Heart Catheterization Heart Defects Congenital Humans Iceland Incidence Infant Newborn Male Registries Retrospective Studies Risk Assessment Severity of Illness Index Sex Distribution Survival Rate |
description |
To access publisher full text version of this article. Please click on the hyperlink in Additional Links field INTRODUCTION AND BACKGROUND: About 1% of live-born children have congenital malformations of the heart. The aim of our study was to investigate the incidence of such defects in children born in Iceland during a period of 10 years, extending from 1990 through 1999. MATERIALS AND METHODS: Information about the patients was obtained from medical records from two hospitals that cover the whole country, a private clinic of pediatric cardiologists, an echocardiography database, autopsy reports, and death certificates. We investigated the distribution of specific malformations, the age at diagnosis, the symptoms leading to the diagnosis, the source of referral, and treatment and quality of life. RESULTS: Between 1990 and 1999, there were 44,013 live births in Iceland, of which 740 patients were diagnosed with congenital cardiac malformations, accounting for 1.7% of the live-born children. The distribution was made up of 338 patients with ventricular septal defect (45.7%), 90 with atrial septal defect (12.2%), 85 with patency of the arterial duct (11.5%), 48 with pulmonary valvar stenosis (6.5%), 38 with a bicuspid aortic valve (5.1%), 28 with aortic coarctation (3.8%), 22 with tetralogy of Fallot (3.0%), 14 with transposed great arteries (1.9%), 11 with aortic stenosis (1.5%), 10 with atrioventricular septal defect and common atrioventricular orifice (1.4%), 9 with mitral valvar regurgitation (1.2%), 7 with sub-aortic stenosis (0.9%), and 5 with hypoplasia of the left heart (0.7%). Extracardiac anomalies were seen in 89 patients (12.0%). Chromosomal defects were seen in 36 patients, of whom 28 had Down's syndrome. DISCUSSION: The annual incidence of diagnosis of patients with congenital cardiac malformations increased during the period of study. This was noted for minor defects, but the incidence of the major anomalies did not alter. Our observed yearly incidence, at 1.7%, was higher than noted in a previous ... |
author2 |
Children's Hospital, University Hospital of Iceland, Hringbraut, Reykjavik, Iceland. |
format |
Article in Journal/Newspaper |
author |
Stephensen, Sigurdur Sverrir Sigfusson, Gunnlaugur Eiriksson, Herbert Sverrisson, Jon Thor Torfason, Bjarni Haraldsson, Asgeir Helgason, Hrodmar |
author_facet |
Stephensen, Sigurdur Sverrir Sigfusson, Gunnlaugur Eiriksson, Herbert Sverrisson, Jon Thor Torfason, Bjarni Haraldsson, Asgeir Helgason, Hrodmar |
author_sort |
Stephensen, Sigurdur Sverrir |
title |
Congenital cardiac malformations in Iceland from 1990 through 1999 |
title_short |
Congenital cardiac malformations in Iceland from 1990 through 1999 |
title_full |
Congenital cardiac malformations in Iceland from 1990 through 1999 |
title_fullStr |
Congenital cardiac malformations in Iceland from 1990 through 1999 |
title_full_unstemmed |
Congenital cardiac malformations in Iceland from 1990 through 1999 |
title_sort |
congenital cardiac malformations in iceland from 1990 through 1999 |
publisher |
Cambridge University Press |
publishDate |
2008 |
url |
http://hdl.handle.net/2336/32892 https://doi.org/10.1017/S1047951104004081 |
genre |
Iceland |
genre_facet |
Iceland |
op_relation |
http://search.ebscohost.com/login.aspx?direct=true&db=aph&AN=16824970&site=ehost-live Cardiol Young 2004, 14(4):396-401 1047-9511 15680046 doi:10.1017/S1047951104004081 http://hdl.handle.net/2336/32892 Cardiology in the young |
op_doi |
https://doi.org/10.1017/S1047951104004081 |
container_title |
Cardiology in the Young |
container_volume |
14 |
container_issue |
4 |
container_start_page |
396 |
op_container_end_page |
401 |
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1766037309964156928 |