Hirschprungs sjúkdómur á Íslandi 1968-1998
Neðst á síðunni er hægt að nálgast greinina í heild sinni með því að smella á hlekkinn View/Open Introduction: Hirschprung s disease (HD) is a congenital disease characterized by the absence of myenteric and submucosal ganglion cells in the distal alimentary tract and results in decreased motility i...
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Læknafélag Íslands, Læknafélag Reykjavíkur
2008
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ftlandspitaliuni:oai:www.hirsla.lsh.is:2336/30213 2023-05-15T16:46:57+02:00 Hirschprungs sjúkdómur á Íslandi 1968-1998 Hirschprung' disease in Iceland 1969-1998 Elísabet S. Guðmundsdóttir Guðmundur Bjarnason Jónas Magnússon Plastikkirurgiska klinikken, Sahlgrenska Universitetssjukhuset, Grœna stråket 8, 413 45 Gothenburg, Sweden elisabetsgud@hotmail.com. 2008-06-19 http://hdl.handle.net/2336/30213 ICE is ice Læknafélag Íslands, Læknafélag Reykjavíkur http://www.laeknabladid.is Læknablaðið 2001, 87(12):987-89 0023-7213 17019022 http://hdl.handle.net/2336/30213 Læknablaðið Hirschprungs sjúkdómur Hirschsprung Disease Article 2008 ftlandspitaliuni 2022-05-29T08:21:09Z Neðst á síðunni er hægt að nálgast greinina í heild sinni með því að smella á hlekkinn View/Open Introduction: Hirschprung s disease (HD) is a congenital disease characterized by the absence of myenteric and submucosal ganglion cells in the distal alimentary tract and results in decreased motility in the affected bowel segment. The purpose of this study was to review the incidence, presentation, treatment and operative results in children with Hirschprung's disease in Iceland. Material and methods: Thirteen infants with Hirschprung s disease (11 boys and two girls) were treated in Landspítalinn University Hospital between January 1969 and December 1998. The records of these patients were reviewed retrospectively. Results: The incidence of Hirschprung's disease in Iceland is 1/10,000 and 85% of those are boys. All the infants were born full term. No family history and no associated abnormalities were noted. The mean age at first admission was 20 (1-136) days and mean age at diagnosis was 166 (5-623) days. Swenson's pull-through (two- or three-stage procedure) was carried out in all patients at the mean age of 18.6 months. The extent of aganglionosis was rectosigmoid colon in 10 patients (77%) and one patient had total colonic aganglionosis. Postoperative complications occurred in seven patients (53%), adhesion ileus being the most common complication. Long term bowel function was satisfactory in 85% of the patients. Conclusions: The incidence of Hirschprung's disease in Iceland is low. Mean age at diagnosis is six months. Sixty percent of the children are discharged with a wrong diagnosis after first admission to hospital and this could be improved by diagnosing the disease at an earlier stage. Postoperative complications are common but no deaths occurred. Bowel function following definitive correction is good compared to other studies. Inngangur: Hirschprungs sjúkdómur er meðfæddur garnasjúkdómur þar sem taugahnoðafrumur (ganglion cells) vantar í vöðvahjúps- (Auerbach) og slímhúðarbeðs- (Meissner) ... Article in Journal/Newspaper Iceland Hirsla - Landspítali University Hospital research archive Smella ENVELOPE(29.443,29.443,69.896,69.896) |
institution |
Open Polar |
collection |
Hirsla - Landspítali University Hospital research archive |
op_collection_id |
ftlandspitaliuni |
language |
Icelandic |
topic |
Hirschprungs sjúkdómur Hirschsprung Disease |
spellingShingle |
Hirschprungs sjúkdómur Hirschsprung Disease Elísabet S. Guðmundsdóttir Guðmundur Bjarnason Jónas Magnússon Hirschprungs sjúkdómur á Íslandi 1968-1998 |
topic_facet |
Hirschprungs sjúkdómur Hirschsprung Disease |
description |
Neðst á síðunni er hægt að nálgast greinina í heild sinni með því að smella á hlekkinn View/Open Introduction: Hirschprung s disease (HD) is a congenital disease characterized by the absence of myenteric and submucosal ganglion cells in the distal alimentary tract and results in decreased motility in the affected bowel segment. The purpose of this study was to review the incidence, presentation, treatment and operative results in children with Hirschprung's disease in Iceland. Material and methods: Thirteen infants with Hirschprung s disease (11 boys and two girls) were treated in Landspítalinn University Hospital between January 1969 and December 1998. The records of these patients were reviewed retrospectively. Results: The incidence of Hirschprung's disease in Iceland is 1/10,000 and 85% of those are boys. All the infants were born full term. No family history and no associated abnormalities were noted. The mean age at first admission was 20 (1-136) days and mean age at diagnosis was 166 (5-623) days. Swenson's pull-through (two- or three-stage procedure) was carried out in all patients at the mean age of 18.6 months. The extent of aganglionosis was rectosigmoid colon in 10 patients (77%) and one patient had total colonic aganglionosis. Postoperative complications occurred in seven patients (53%), adhesion ileus being the most common complication. Long term bowel function was satisfactory in 85% of the patients. Conclusions: The incidence of Hirschprung's disease in Iceland is low. Mean age at diagnosis is six months. Sixty percent of the children are discharged with a wrong diagnosis after first admission to hospital and this could be improved by diagnosing the disease at an earlier stage. Postoperative complications are common but no deaths occurred. Bowel function following definitive correction is good compared to other studies. Inngangur: Hirschprungs sjúkdómur er meðfæddur garnasjúkdómur þar sem taugahnoðafrumur (ganglion cells) vantar í vöðvahjúps- (Auerbach) og slímhúðarbeðs- (Meissner) ... |
author2 |
Plastikkirurgiska klinikken, Sahlgrenska Universitetssjukhuset, Grœna stråket 8, 413 45 Gothenburg, Sweden elisabetsgud@hotmail.com. |
format |
Article in Journal/Newspaper |
author |
Elísabet S. Guðmundsdóttir Guðmundur Bjarnason Jónas Magnússon |
author_facet |
Elísabet S. Guðmundsdóttir Guðmundur Bjarnason Jónas Magnússon |
author_sort |
Elísabet S. Guðmundsdóttir |
title |
Hirschprungs sjúkdómur á Íslandi 1968-1998 |
title_short |
Hirschprungs sjúkdómur á Íslandi 1968-1998 |
title_full |
Hirschprungs sjúkdómur á Íslandi 1968-1998 |
title_fullStr |
Hirschprungs sjúkdómur á Íslandi 1968-1998 |
title_full_unstemmed |
Hirschprungs sjúkdómur á Íslandi 1968-1998 |
title_sort |
hirschprungs sjúkdómur á íslandi 1968-1998 |
publisher |
Læknafélag Íslands, Læknafélag Reykjavíkur |
publishDate |
2008 |
url |
http://hdl.handle.net/2336/30213 |
long_lat |
ENVELOPE(29.443,29.443,69.896,69.896) |
geographic |
Smella |
geographic_facet |
Smella |
genre |
Iceland |
genre_facet |
Iceland |
op_relation |
http://www.laeknabladid.is Læknablaðið 2001, 87(12):987-89 0023-7213 17019022 http://hdl.handle.net/2336/30213 Læknablaðið |
_version_ |
1766037038301184000 |