Creutzfeldt–Jakob disease in the Republic of Sakha (Yakutia)

• Published in: Neurology, Neuropsychiatry, Psychosomatics
• Main Authors: T. E. Popova, A. A. Tappakhov, T. K. Davydova, T. Ya. Nikolaeva, Yu. I. Khabarova, M. A. Varlamova, L. T. Okoneshinova, Т. Е. Попова, А. А. Таппахов, Т. К. Давыдова, Т. Я. Николаева, Ю. И. Хабарова, М. А. Варламова, Л. Т. Оконешникова
• Format: Article in Journal/Newspaper
• Language: Russian; English
• Published: "IMA-Press", LLC 2020
• Subjects: губчатые энцефалопатии; Creutzfeldt–Jakob disease; dementia; myoclonus; spongiform encephalopathies; болезнь Крейтцфельда–Якоба; деменция; миоклонии; Sakha; Venus; Republic of Sakha; Yakutia; Саха; Якути*; Якутия
• Online Access: https://nnp.ima-press.net/nnp/article/view/1310; https://doi.org/10.14412/2074-2711-2020-2-86-91

Creutzfeldt–Jakob disease (CJD) is a rare neurodegenerative disease caused by the accumulation of the pathological isoform of prion protein. The classic clinical presentation of CJD is characterized by rapidly progressive dementia, ataxia, myoclonus, and akinetic mutism at the terminal stage of the...