Family Clustering of Viliuisk Encephalomyelitis in Traditional and New Geographic Regions
Viliuisk encephalomyelitis is an acute, often fatal, meningoencephalitis that tends to develop into a prolonged chronically progressive panencephalitis. Clinical, neuropathologic, and epidemiologic data argue for an infectious cause, although multiple attempts at pathogen isolation have been unsucce...
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ftcdc:oai:example.org:cdc:16662 2023-05-15T16:08:58+02:00 Family Clustering of Viliuisk Encephalomyelitis in Traditional and New Geographic Regions Emerg Infect Dis Vladimirtsev, Vsevolod A. Nikitina, Raisa S. Renwick, Neil Ivanova, Anastasia A. Danilova, Al’bina P. Platonov, Fyodor A. Krivoshapkin, Vadim G. McLean, Catriona A. Masters, Colin L. Gajdusek, D. Carleton Goldfarb, Lev G. http://stacks.cdc.gov/view/cdc/16662/ unknown http://stacks.cdc.gov/view/cdc/16662/ Emerg Infect Dis. 13(9):1321-1326. Research Viliuisk encephalomyelitis Yakut (Sakha) people Siberia Viliui River Familial aggregation Adolescent Adult Encephalomyelitis Family Female Humans Male Middle Aged ftcdc 2017-04-11T13:16:29Z Viliuisk encephalomyelitis is an acute, often fatal, meningoencephalitis that tends to develop into a prolonged chronically progressive panencephalitis. Clinical, neuropathologic, and epidemiologic data argue for an infectious cause, although multiple attempts at pathogen isolation have been unsuccessful. To assess mechanisms of disease transmission and spread, we studied 6 multiplex families. Secondary cases occurred among genetically related and unrelated persons in a setting of prolonged intrahousehold contact with a patient manifesting the disease. Transmission to unrelated persons was documented in a densely populated region around the city of Yakutsk in which Viliuisk encephalomyelitis had not been previously known. Initially identified in a small Yakut-Evenk population on the Viliui River of eastern Siberia, the disease subsequently spread through human contacts to new geographic areas, thus characterizing Viliuisk encephalomyelitis as an emerging infectious disease. Other/Unknown Material Evenk Sakha Yakut Yakutsk Siberia CDC Stacks (Centers for Disease Control and Prevention) Sakha Yakutsk |
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CDC Stacks (Centers for Disease Control and Prevention) |
op_collection_id |
ftcdc |
language |
unknown |
topic |
Research Viliuisk encephalomyelitis Yakut (Sakha) people Siberia Viliui River Familial aggregation Adolescent Adult Encephalomyelitis Family Female Humans Male Middle Aged |
spellingShingle |
Research Viliuisk encephalomyelitis Yakut (Sakha) people Siberia Viliui River Familial aggregation Adolescent Adult Encephalomyelitis Family Female Humans Male Middle Aged Family Clustering of Viliuisk Encephalomyelitis in Traditional and New Geographic Regions |
topic_facet |
Research Viliuisk encephalomyelitis Yakut (Sakha) people Siberia Viliui River Familial aggregation Adolescent Adult Encephalomyelitis Family Female Humans Male Middle Aged |
description |
Viliuisk encephalomyelitis is an acute, often fatal, meningoencephalitis that tends to develop into a prolonged chronically progressive panencephalitis. Clinical, neuropathologic, and epidemiologic data argue for an infectious cause, although multiple attempts at pathogen isolation have been unsuccessful. To assess mechanisms of disease transmission and spread, we studied 6 multiplex families. Secondary cases occurred among genetically related and unrelated persons in a setting of prolonged intrahousehold contact with a patient manifesting the disease. Transmission to unrelated persons was documented in a densely populated region around the city of Yakutsk in which Viliuisk encephalomyelitis had not been previously known. Initially identified in a small Yakut-Evenk population on the Viliui River of eastern Siberia, the disease subsequently spread through human contacts to new geographic areas, thus characterizing Viliuisk encephalomyelitis as an emerging infectious disease. |
author2 |
Vladimirtsev, Vsevolod A. Nikitina, Raisa S. Renwick, Neil Ivanova, Anastasia A. Danilova, Al’bina P. Platonov, Fyodor A. Krivoshapkin, Vadim G. McLean, Catriona A. Masters, Colin L. Gajdusek, D. Carleton Goldfarb, Lev G. |
title |
Family Clustering of Viliuisk Encephalomyelitis in Traditional and New Geographic Regions |
title_short |
Family Clustering of Viliuisk Encephalomyelitis in Traditional and New Geographic Regions |
title_full |
Family Clustering of Viliuisk Encephalomyelitis in Traditional and New Geographic Regions |
title_fullStr |
Family Clustering of Viliuisk Encephalomyelitis in Traditional and New Geographic Regions |
title_full_unstemmed |
Family Clustering of Viliuisk Encephalomyelitis in Traditional and New Geographic Regions |
title_sort |
family clustering of viliuisk encephalomyelitis in traditional and new geographic regions |
url |
http://stacks.cdc.gov/view/cdc/16662/ |
geographic |
Sakha Yakutsk |
geographic_facet |
Sakha Yakutsk |
genre |
Evenk Sakha Yakut Yakutsk Siberia |
genre_facet |
Evenk Sakha Yakut Yakutsk Siberia |
op_source |
Emerg Infect Dis. 13(9):1321-1326. |
op_relation |
http://stacks.cdc.gov/view/cdc/16662/ |
_version_ |
1766404973465174016 |